Clinical Management of Glanzmann's Thrombasthenia: A Case Report.

Indu Varkey; Kavita Rai; Amitha M Hegde; Mangalpady Shenoy Vijaya; Vinod Idicula Oommen

Indu Varkey Post Graduate Student, A. B Shetty Memorial Institute of Dental Sciences, Mangalore, India.
Kavita Rai Professor, Department of Pedodontics and Preventive Dentistry, A.B Shetty Memorial Institute of Dental Sciences, Mangalore, India.
Amitha M Hegde Professor, Department of of Pedodontics and Preventive Dentistry, A.B Shetty Memorial Institute of Dental Sciences, Mangalore, India.
Mangalpady Shenoy Vijaya Professor, Department of Pediatrics, K.S. Hegde Medical Academy, Mangalore, India.
Vinod Idicula Oommen Post Graduate Student, Department of Pediatrics, K.S. Hegde Medical Academy, Mangalore, India.

Keywords:

Complete Oral Rehabilitation, Glanzmann’s Thrombasthenia, Platelet Disorder

Abstract

Glanzmann's thrombasthenia (GT) is a rare, genetically inherited platelet disorder in which the platelet glycoprotein IIb/IIIa (GP IIb/IIIa) complex is either deficient or, dysfunctional. The incidence is about 1 in 1,000,000. This case report deals with a 4 year-old girl diagnosed with GT presenting with dental caries and periapical lesions in the primary mandibular first molars. To provide the best care, an interdisciplinary approach was followed by a team consisting of pediatric dentists, pediatricians and anesthesiologists. Complete oral rehabilitation was planned under general anesthesia which included extractions, multiple esthetic restorations and space maintainers with the utmost care to prevent unwarranted bleeding.